Congenital fibrosarcoma is a rare fibrous tissue malignancy occurring most commonly in the extremities (71%), but presenting in axial locations as well (29%).                                    Congenital fibrosarcoma is unique among human sarcomas in that it has an excellent prognosis and very low metastatic rate.                                         It differs from the fibrosarcoma in adulthood by its clinical behaviour: the clinical course of congenital  fibrosarcoma is more favorable and metastatic spread is rare. Localization also differs: while adult fibrosarcomas are common in the thigh, congenital  fibrosarcomas affect chiefly the distal portions of the extremities. [ Back ]